This book describes Hyperacusis (Hypersensitivity to Sound), Diagnosis and Treatment and Related Diseases

Hyperacusis is a hearing disorder that makes it difficult to manage everyday sounds.

The patient might also called it sound or noise hypersensitivity.

If the patient has it, certain sounds may appear unbearably loud even though people around the patient do not appear to notice them.

Hyperacusis is a disorder of loudness perception, where sounds that are ordinarily considered normal become intolerable.

Patients may feel this sensation as painful, frightening, unpleasant, or excessively loud.

Hyperacusis is rare.

It affects 1 in 50,000 people.

People who have it also have another disorder called tinnitus which is buzzing or ringing in the ear.

Hyperacusis often co-exists with tinnitus and can cause considerable distress, with patients regularly reporting reduction in their social, occupational, and recreational activities.

Avoiding sound sources in Hyperacusis and seeking medical attention are frequent behaviors.

The terms phonophobia (fear of sound) and misophonia (hatred of sound) can be linked with intolerance to specific sounds and may have an emotional component with the former mostly linked with migraine.

While a definitive cure is yet to be identified, research in this field is increasing, and there has been a 10-fold increase in the number of peer-reviewed studies on the disorder in the past 4 decades.

People are not typically born with hyperacusis.

It normally results from certain diseases or health disorders.

The most frequent causes are:

1. An injury to the head (one caused by a knock on the head)
2. Damage to one or both ears because of medications or toxins
3. A viral infection that affects the inner ear or facial nerve (Bell's palsy)
4. Temporomandibular joint (TMJ) disorder
5. Lyme disease
6. Tay-Sachs disease
7. Migraine headaches
8. Using Valium regularly
9. Certain kinds of epilepsy
10. Chronic fatigue syndrome
11. Meniere's disease
12. Posttraumatic stress disorder (PTSD)
13. Depression
14. Autism
15. Surgery on the jaw or face
16. Williams syndrome

The most frequent cause of hyperacusis is high noise exposure without hearing protection.

Exposure to a loud noise also can produce hyperacusis.

Some sound such as a single loud gunshot can trigger the disorder.

But it also can result from being near loud noises over a long period.

Phonophobia and misophonia are disorders linked with the limbic system in the brain and there is no abnormality in the peripheral or central auditory system.

Phonophobia is a psychiatric disorder where there is a fear of a definite sound.

Misophonia is a psychological disorder in which a specific sound activates emotional and physical reactions.

Hyperacusis is the sound sensitivity developing from within the auditory system and can be activated by any generic, low-intensity sound.

The diagnosis of hyperacusis involves determining LDL using pure-tone audiometry and questionnaires to determine disease severity.

Cognitive-behavioral therapy (CBT) is one of the most effective parts of hyperacusis therapy together with counseling and education.

Tinnitus retraining therapy (TRT) involves educating the patient about their disorder alongside gradual sound enrichment.

Prolonged low-level noise exposure has been proven to have a reversing effect on the enhanced neural gain, which is believed to be the underlying mechanism of hyperacusis.

TABLE OF CONTENT
Introduction
Chapter 1...